Display options
Cite
Nishikawa T, Tanaka Y, Sasaki Y, et al. A case of pediatric cardiomyopathy with severely restrictive physiology. Heart Vessels. 1992;7(4):206-10doi: 10.1007/BF01744606.
Nishikawa, T., Tanaka, Y., Sasaki, Y., Kawataki, M., Miyazawa, Y., Yasui, S., Takarada, M., & Kasajima, T. (1992). A case of pediatric cardiomyopathy with severely restrictive physiology. Heart and vessels, 7(4), 206-10. https://doi.org/10.1007/BF01744606
Nishikawa, T, et al. "A case of pediatric cardiomyopathy with severely restrictive physiology." Heart and vessels vol. 7,4 (1992): 206-10. doi: https://doi.org/10.1007/BF01744606
Nishikawa T, Tanaka Y, Sasaki Y, Kawataki M, Miyazawa Y, Yasui S, Takarada M, Kasajima T. A case of pediatric cardiomyopathy with severely restrictive physiology. Heart Vessels. 1992;7(4):206-10. doi: 10.1007/BF01744606. PMID: 1487458.
Copy Download .nbib Format: NLM
Share it on

Heart Vessels. 1992;7(4):206-10. doi: 10.1007/BF01744606.

A case of pediatric cardiomyopathy with severely restrictive physiology.

Heart and vessels

T Nishikawa, Y Tanaka, Y Sasaki, M Kawataki, Y Miyazawa, S Yasui, M Takarada, T Kasajima

Affiliations

  1. Department of Pathology, Tokyo Women's Medical College, Japan.

PMID: 1487458 DOI: 10.1007/BF01744606

Abstract

A rare case of a 6-year-old male with idiopathic familial cardiomyopathy manifesting severely restrictive physiology is reported. The patient showed congestive heart failure with dilatation of both atria with a normal ventricular cavity. A square-root configuration was revealed in the ventricular pressure tracings. His elder brother had died of hypertrophic cardiomyopathy at the age of 3 years. Endomyocardial biopsy disclosed marked disorganization of muscle bundles with hypertrophy of the myocytes and interstitial fibrosis. The patient died suddenly during hospitalization. Autopsy revealed diffuse hypertrophy of both the ventricular walls and the ventricular septum with extensive myocardial disorganization and interstitial fibrosis. These advanced myopathic changes in the myocardium may have been related to the restrictive physiology in this case.

Similar articles

Show all 11 similar articles

References

  1. N Engl J Med. 1989 Nov 16;321(20):1372-8 - PubMed
  2. Lancet. 1971 Nov 13;2(7733):1065-7 - PubMed
  3. Am Heart J. 1981 Oct;102(4):790-2 - PubMed
  4. Circulation. 1984 Aug;70(2):165-9 - PubMed
  5. Chest. 1983 Aug;84(2):236-8 - PubMed
  6. Heart Vessels. 1985 Aug;1(3):170-5 - PubMed
  7. Am J Hum Genet. 1990 Sep;47(3):389-94 - PubMed
  8. Circulation. 1978 Mar;57(3):512-20 - PubMed

MeSH terms

Publication Types

LinkOut - more resources